II. Physiology
- Cholesterol is precursor for 5 steroid hormone classes
- Progestagens (e.g. Progesterone)
- Glucocorticoids (e.g. Cortisol)
- Mineralcorticoids (e.g. Aldosterone)
- Androgens (e.g. Testosterone)
- Estrogens
- Synthesis sites
- Conditions related to enzyme deficiencies
- Congenital Adrenal Hyperplasia
- 21-Hydroxylase deficiency is most common
- Congenital Adrenal Hyperplasia
III. Step 1: Steroid Synthesis – Cholesterol to Precursors
- Cholesterol converted to Pregnenolone
- Stimulated by ACTH release from anterior pituitary
- Key enzyme: Desmolase
- Pregnenolone converted to Progesterone
- Pregnenolone is precursor of all steroids
- Key enzyme: 3-B-Hydroxysteroid Dehydrogenase
- Progesterone converted to 17-a-hydroxyprogesterone
- Key enzyme: 17-Hydroxylase
- 17-a-hydroxyprogesterone is precursor
- Cortisol Synthesis (Go to step 2)
- Aldosterone Synthesis (Go to Step 4)
- 17-a-hydroxyprogesterone converted to Androstenedione
- Key enzyme: 3-B-Hydroxysteroid Dehydrogenase
- Androstenedione is sex hormone precursor (see Step 3)
- Estrone
- Testosterone
- Estradiol
IV. Step 2: Cortisol Synthesis from 17-a-hydroxyprogesterone
- 17-a-hydroxyprogesterone converted to 11-Deoxycortisol
- Key enzyme: 21-Hydroxylase
- Most common enzyme deficiency in steroid synthesis
- 11-Deoxycortisol converted to Cortisol
- Key enzyme: 11-Hydroxylase
- Enzyme deficiency related condition
- Cortisol
V. Step 3: Sex Hormones from Androstenedione
- Androstenedione converted to Estrone or
- Androstenedione converted to Testosterone
- Testosterone converted to Estradiol
VI. Step 4: Aldosterone from Progesterone
- Progesterone converted to 11-Deoxycorticosterone
- Key enzyme: 21-Hydroxylase
- 11-Deoxycorticosterone converted to Cortisosterone
- Key enzyme: 11-Hydroxylase
- Corticosterone converted to Aldosterone